A medical food powder for children and adults with homocystinuria.
Last Updated: Monday, October 5, 2015
Indication: HCY 2 is a medical food powder that is free of the essential amino acid methionine for children and adults with homocystinuria. The product provides all other essential amino acids as well as nonessential amino acids, carbohydrate, fat, essential fatty acids, vitamins and minerals. Use under direct and continuing supervision of a doctor.
Cystine level is similar to the sum of cystine and methionine found in cow's milk
22 g protein equivalents/100 g powder
Suitable for someone with lactose intolerance
Can be easily modified with preferred flavor enhancers
Mixes easily and stays in suspension well
Vitamin and mineral levels appropriate for children and adults
|Per 100 grams Powder|
|Protein equivalent, g†||22|
|Linoleic acid, mg||4200|
|Linolenic acid, mg||520|
|Per 100 grams Powder|
|Vitamins ⁄ Other Nutrients|
|Vitamin A, IU||1730|
|Vitamin D, IU||350|
|Vitamin E, IU||12.2|
|Vitamin K, mcg||47|
|Thiamin (Vitamin B1), mcg||1430|
|Riboflavin (Vitamin B2), mcg||1140|
|Vitamin B6, mcg||1140|
|Vitamin B12, mcg||2.9|
|Folic acid (Folacin), mcg||410|
|Pantothenic acid, mcg||5700|
|Vitamin C (Ascorbic acid), mg||57|
|Per 100 grams Powder|
* Product nutrient values and ingredients are subject to change. Please see product label for current information. † Protein is incomplete since it does not contain the essential amino acid methionine.
|Protein Equivalent (% Calories)†||22|
|Fat (% Calories)||19|
|Carbohydrate (% Calories)||59|
|Lactose-Free||Suitable for someone with lactose intolerance|
† Protein is incomplete since it does not contain the essential amino acid methionine.
HCY 2 is available in powder.
Item #: 891901
Unit Size: 1 lb can
Prod. Yield / Unit (fl oz): Varies
Case: 6 cans per case
HCPCS Code: B4157 or B4162
Reimbursement Code: N/A
Ingredients: Corn syrup solids, amino acids (L-glutamine, L-leucine, L-lysine hydrochloride, potassium aspartate, L-proline, L-valine, L-isoleucine, L-alanine, L-arginine, L-threonine, L-phenylalanine, L-tyrosine, L-serine, L-cystine, glycine, L-histidine, L-tryptophan), sugar, soy oil, modified corn starch, calcium phosphate, sodium citrate, magnesium phosphate, potassium chloride, and less than 1%: sodium phosphate, potassium citrate, choline chloride, ascorbic acid, taurine, inositol, ferrous sulfate, L-carnitine, zinc sulfate, niacinamide, vitamin E acetate, vitamin A palmitate, calcium pantothenate, cupric sulfate, manganese sulfate, vitamin B12, thiamin hydrochloride, vitamin B6 hydrochloride, riboflavin, folic acid, vitamin D3, chromic chloride, sodium molybdate, sodium selenite, sodium iodide, biotin, vitamin K1, ethyl vanillin.
Metabolic clinician should consult with patients about the correct amounts of water and powder for consumption. The patient's health depends on carefully following these directions.
Measure the correct amount of water into a suitable container for mixing. Then add the required amount of HCY 2. Mix well until blended. Consume the prepared beverage immediately or cover and refrigerate. Use within 48 hours of preparation. Mix before drinking.
Throw away prepared unrefrigerated beverage left in cup within 1 hour after consumption begins.
Powder Storage (cans)
Store cans at room temperature. After opening can, keep tightly covered, store in a dry area and use contents within 1 month. Do not freeze powder, and avoid excessive heat. Use by date on bottom of can.
An unpacked level scoop delivers approximately 14.5 g of powder. Store the DRY scoop in this can.
This product is nutritionally incomplete. Continuing medical supervision and frequent blood tests are required. Care must be taken to provide enough methionine to support growth, using other foods with this amino acid as required.
Nutritional powders are not sterile.
WARNING: Not for parenteral (I.V.) use.
Fat provides 19% of total calories in HCY 2. The fat source is soy oil. Soy oil is a source of essential omega-6 and omega-3 fatty acids: linoleic acid and alpha-linolenic acid.
Protein equivalents provide 22% of total calories in HCY 2. The product provides the essential amino acids (except methionine) as well as nonessential amino acids (see Amino Acids table). Since the product is methionine-free, care must be taken to provide enough methionine from other foods to support growth and tissue maintenance. The high protein equivalent concentration in HCY 2 helps persons with homocystinuria meet their protein needs while consuming fewer calories from the product. This, in turn, allows HCY 2 users to consume a greater variety of foods in order to meet their methionine and calorie needs.
|Essential Amino Acids||Per 100 g Powder|
|Nonessential Amino Acids||Per 100 g Powder|
|Aspartic acid, mg||1760|
|Glutamic acid, mg||3500‡|
‡ Added as glutamine.
Carbohydrate provides 59% of total calories in HCY 2. The carbohydrate blend is 52% corn syrup solids, 41% sucrose (table sugar) and 7% modified corn starch. The sucrose in the product helps mask the taste of the amino acids. HCY 2 is suitable for someone with lactose intolerance.
Vitamins and Minerals
HCY 2 provides essential vitamins and minerals at levels that are appropriate for children and adults.