• A medical food powder for children and adults with homocystinuria.

HCY 2

A medical food powder for children and adults with homocystinuria.

Last Updated: Wednesday, December 27, 2017

  • Description/Indication
    • HCY 2 is a medical food powder that is free of the essential amino acid methionine for children and adults with documented homocystinuria. The product provides all other essential amino acids as well as nonessential amino acids, carbohydrate, fat, essential fatty acids, vitamins and minerals. Use under direct and continuing supervision of a doctor.

  • Product Features
      • Methionine-free
      • Cystine level is similar to the sum of cystine and methionine found in cow’s milk
      • 22 g protein equivalent/100 g powder
      • Suitable for someone with lactose intolerance
      • Vanilla scent
      • Can be easily modified with preferred flavor enhancers
      • Mixes easily and stays in suspension well
      • Vitamin and mineral levels appropriate for children and adults
      • Halal
  • Nutrients
    • Product nutrient values and ingredients are subject to change. Please see product label for current information.

      Per 100 grams Powder
      Calories 410
      Protein equivalent, g* 22
      Fat, g 8.5
      Linoleic acid, mg 4200
      Carbohydrate, g 61
      Per 100 grams Powder
      Vitamins ⁄ Other Nutrients
      Vitamin A, IU 1730
      Vitamin D, IU 350
      Vitamin E, IU 12.2
      Vitamin K, mcg 47
      Thiamin (Vitamin B1), mcg 1430
      Riboflavin (Vitamin B2), mcg 1140
      Vitamin B6, mcg 1140
      Vitamin B12, mcg 2.9
      Niacin, mcg 26000
      Folic acid (Folacin), mcg 410
      Pantothenic acid, mcg 5700
      Biotin, mcg 57
      Vitamin C (Ascorbic acid), mg 57
      Choline, mg 98
      Inositol, mg 57
      Per 100 grams Powder
      Minerals
      Calcium, mg 730
      Phosphorus, mg 730
      Magnesium, mg 163
      Iron, mg 13.8
      Zinc, mg 13.8
      Manganese, mcg 1500
      Copper, mcg 1430
      Iodine, mcg 63
      Selenium, mcg 33
      Chromium, mcg 45
      Molybdenum, mcg 45
      Sodium, mg 590
      Potassium, mg 1100
      Chloride, mg 960

      * WARNING: Protein is incomplete since it does not contain the essential amino acid methionine.

  • Nutrient Facts
    • Protein Equivalent (% Calories) 22
      Fat (% Calories) 19
      Carbohydrate (% Calories) 59
      Lactose-Free Suitable for someone with lactose intolerance

      * WARNING: Protein is incomplete since it does not contain the essential amino acid methionine.

  • Product Form
    • HCY 2 is available in powder.

      Item #: 891901
      Description: Powder
      Unit Size: 1 lb can
      Cal./Unit: 1860
      Prod. Yield / Unit (fl oz): Varies
      Case: 6 cans per case
      HCPCS Code: B4157 or B4162
      Reimbursement Code: 00087-510027

      HCPCS Code

  • Composition
    • Ingredients: Corn syrup solids, amino acids (L-glutamine, L-leucine, L-lysine hydrochloride, potassium aspartate, L-proline, L-valine, L-isoleucine, L-alanine, L-arginine, L-threonine, L-phenylalanine, L-tyrosine, L-serine, L-cystine, glycine, L-histidine, L-tryptophan), sugar, soy oil, modified corn starch, calcium phosphate, sodium citrate, magnesium phosphate, potassium chloride and less than 1%: sodium phosphate, potassium citrate, choline chloride, ascorbic acid, taurine, inositol, ferrous sulfate, L-carnitine, zinc sulfate, niacinamide, vitamin E acetate, vitamin A palmitate, calcium pantothenate, cupric sulfate, manganese sulfate, vitamin B12, thiamin hydrochloride, vitamin B6 hydrochloride, riboflavin, folic acid, vitamin D3, chromic chloride, sodium molybdate, sodium selenite, sodium iodide, biotin, vitamin K1, ethyl vanillin.

      CAUTION: Mead Johnson Nutrition HCY 2 is to be used only in the dietary management of children and adults with documented homocystinuria while under direct and continuing medical supervision.

      WARNING: This product is nutritionally incomplete. Continuing medical supervision and frequent blood tests are required. HCY 2 must be supplemented using other food sources of protein and fluid to provide enough methionine to support dietary requirements of children and adults.

      WARNING: Not for parenteral (I.V.) use.

  • Preparation of Feedings
    • The medical professional will provide the correct amount of powder to mix with water for consumption.

      It is important to follow the directions below.

      Measure the correct amount of water into a suitable container for mixing. Then add the required amount of product. Mix well until blended. Consume the prepared beverage immediately or cover and refrigerate. Use within 48 hours of preparation. Mix before drinking.

      If instructed to use the scoop in the can, see the chart below for weight of one unpacked, level scoop of product. Store DRY scoop in can.

      Weight—one unpacked, level scoop (g)

             
      BCAD 2 14.5 Phenyl-Free 2 14.4
      HCY 2 14.5 Phenyl-Free 2 HP 15.1
      OA 2 14.5 TYROS 2 14.5
      PFD Toddler 4.5 WND 2 14.5
      PFD 2 14.9
  • Product Characteristics
    • Fat

      Fat provides 19% of total calories in HCY 2. The fat source is soy oil. Soy oil is a source of essential omega-6 and omega-3 fatty acids: linoleic acid and alpha-linolenic acid.

      Protein

      Protein equivalents provide 22% of total calories in HCY 2. The product provides the essential amino acids (except methionine) as well as nonessential amino acids (see Amino Acids table). Since the product is methionine-free, care must be taken to provide enough methionine from other foods to support growth and tissue maintenance. The high protein equivalent concentration in HCY 2 helps persons with homocystinuria meet their protein needs while consuming fewer calories from the product. This, in turn, allows HCY 2 users to consume a greater variety of foods in order to meet their methionine and calorie needs.

      Essential Amino Acids Per 100 g Powder
      Histidine, mg 550
      Isoleucine, mg 1560
      Leucine, mg 2900
      Lysine, mg 1780
      Methionine, mg 0
      Cystine, mg 810
      Phenylalanine, mg 920
      Tyrosine, mg 920
      Threonine, mg 1030
      Tryptophan, mg 420
      Valine, mg 1720
      Nonessential Amino Acids Per 100 g Powder
      Arginine, mg 1340
      Alanine, mg 1450
      Aspartic acid, mg 1760
      Glutamic acid, mg 3500
      Glycine, mg 790
      Proline, mg 1760
      Serine, mg 880

      ‡ Added as glutamine.

      Carbohydrate

      Carbohydrate provides 59% of total calories in HCY 2. The carbohydrate blend is 52% corn syrup solids, 41% sucrose (table sugar) and 7% modified corn starch. The sucrose in the product helps mask the taste of the amino acids. HCY 2 is suitable for someone with lactose intolerance.

      Vitamins and Minerals

      HCY 2 provides essential vitamins and minerals at levels that are appropriate for children and adults.